[SCD-FORUM] 8E 一例肥厚性心肌病失代偿期（burned-out phase）的女性患者 Dr. Alizadeh

[SCD Symposium]

8E 一例肥厚性心肌病失代偿期（burned-out phase）的女 
性患者   Dr. Alizadeh



亲爱的Dr. Dubner，



非常感谢您的这个优秀的教育点。



有一位38岁的妇女在一个月前因为新发的呼吸困难到 
我中心就诊。她有心源性猝死的家族史。她有完全性 
心脏传导阻滞合并室性逸搏心律。经胸超声心动图发 
现严重左室和右室的收缩功能不全，不对称得室间隔 
肥厚，肺动脉高压（PAP = 65-70mmHg），没有左室流出道 
的梗阻。患者呼吸困难的症状在心剂量利尿剂、ACEI 
和临时起搏器植入后仍然加重。

您建议为这位患者植入DDD起搏器？

还是

您建议进行ICD-DR或ICD-CRT治疗？

您对她的疾病的临床过程又什么见解？

她在起搏器植入前还需要什么样的准备？



真诚地，



Hormoz Alizadeh MD
Department of Pacemaker and Electrophysiology
Rajaie Cardiovascular Medical and Research Center
Tehran, Iran




Dear Dr Dubner

     thank you for this excellent  educational site

     A 38 year old femal referred to our center with new onset  
dyspnea from a few month ago. She had family history of sudden cardia  
death. She had CHB with wide ventricular escape rhythm.  
TT.echocardiography revealed sever LV and RV systolic dysfunction,  
asymetric septal hyperthrophy, pulmonary hypertention (PAP=65-70mmhg)  
and without LVOT gradient. patient,s dyspnea improved with low dose  
diuretics , ACE inhibitor and TPM implantation.
     Do you recommend DDD pacemaker for this patient?
     or
     Do you recommend  ICD-DR or ICD-CRT?
     what is your opinion about clinical course of her disease?
     does she need further workup before device implantation?


     sincerely yours

     Hormoz Alizadeh MD
     Department of Pacemaker and Electrophysiology
  Rajaie Cardiovascular Medical and Research Center
  Tehran, Iran


--
Dr. Sergio Dubner
President of Scientific Committee

Dr. Edgardo Schapachnik
President of Steering Committee