[SCD-FORUM] 3E. A children with LQTS. Dr. Haghjoo

[SCD Symposium]

Dear Dr. Dubner,

Thank you and your colleagues for this nice online symposium.  
Recently, a
5-year-old children with no evidence of structural heart disease  
referred to
our center for evaluation of syncope. He also had history of congenital
deafness. One of the episodes of syncope occurred 48-hrs after  
betablocker
withdrawal and second episodes on 10 mg propranolol tid. Surface ECG
revealed a QTc=600 ms and heart rate of 55 bpm. We think that onset in
childhood, congenital deafness and QTc=600 would place this patient at
higher risk for cardiac events and therefore a candidate for ICD
implantation. However, small body size and future risk of inappropriate
therapy with its devastating consequences are unfavorable aspects of ICD
implantation. Our limitimg factors for increase in dose of  
betablocker is
low baseline hear rate. What is recommendation of scientific  
committee of
SCD symposium regarding our patient?

Thank you in advance for your recommendation.

Regards,

Majid Haghjoo,MD
Department of Pacemaker and Electrophysiology
Rajaie Cardiovascular Medical and Research Center
Tel: +98 21 2392 2931
Fax:+98 21 2204 8174
Tehran, Iran