[SCD-FORUM] 61S 一位心脏猝死患者的儿子发现Brugada综合症表现 Cagnalotti 医师

[SCD Symposium]

61S 一位心脏猝死患者的儿子发现Brugada综合症表现  
Cagnalotti 医师
亲爱的 Sergio ：
关于一个猝死后复苏的病例，患者54岁经所有的检查 
包括冠脉造影、磁共振（MNR）, 动态心电图（Holtr）, 
电生理检查（ EPS）均未发现有器质性心脏病。

所有资料显示均正常。患者入院当时检查发现单形性 
心律失常发作。给予患者生命支持，于24小时后恢 
复。决定对其植入ICD。3个月后记录显示由持续性室 
速引发的3次晕厥，并决定在流出道进行标测和局灶 
消融。

直到现在，患者没有显示任何心律失常事件。现在已 
经有3个月了，在他的一个儿子的Holter记录中发现典 
型的Brugada综合征。患者17岁，没有症状。我不能进行 
药理实验。下一步我该如何做？

Sergio Dubner医师
科委会主席
Edgardo Schapachnik医师
组委会主席

刘莹译 王玲洁校

61S Brugada's pattern detection in a son of SCD's patient. Dr.  
Cagnalotti
Dear Sergio,
About a case of reanimation of sudden death in a 54-year-old patient,
with no structural heart disease, with all the studies made: coronary
angiography, MNR, Holter, EPS.
Everything appears to be normal. Monomorphic arrhythmic storm is
detected at the moment the patient is admitted. The patient is
provided life support and he recovers in 24 hs. ICD implantation is
decided. After three months he displays three shocks by arrhythmic
storm, incessant ventricular tachycardia. Mapping and focus ablation
is decided, in outflow tract with mismatch.
To this moment, the patient has not displayed any event. It's been
three months, and in a Holter register in one of his sons, typical
Brugada pattern is observed. The patient is 17 years old,
asymptomatic. I cannot perform pharmacological test. What should I do
next?

Dr. Cagnolatti  <drcagnolattia at hotmail.com>

--
Dr. Sergio Dubner
President of Scientific Committee

Dr. Edgardo Schapachnik
President of Steering Committee