[SCD-FORUM] 33E RE一例患长QT综合征年轻女性-- Klingenheben医师

[SCD Symposium]

33E RE一例患长QT综合征年轻女性-- Klingenheben医师
很有意思的病例，我有一个类似患者，也有产后的室 
颤-心脏骤停,证实是   尖端扭转型室速，采用了ICD 
（植入型心律转复除颤仪）治疗。产后心脏骤停，连 
同T波“切迹”，几乎是2型长QT患者的特征性表现。 
我认为这样的特殊患者以后发生心血管事件的危险性 
很高，我非常支持ICD治疗――不考虑将来怀孕与否。
我想请教Priori教授一个问题：在登记在册的长QT综合 
征患者当中，您是否有那些妊娠期/产后的可疑的/已 
确定的长QT的患者的发生心律失常的临床资料？
Sergio Dubner博士

科委会主席--
Edgardo Schapachnik 博士
组委会主席

Thomas Klingenheben, MD
Assistant Professor of Medicine
Kardiologische Gemeinschaftspraxis
Alfred-Bucherer-Str. 6
D 53115  Bonn - Germany
e-mail: Klingenheben at aol.com
e-mail: Klingenheben at em.uni-frankfurt.de
Web:    www.bonn-kardiologie.de

33E RE: Young woman with LQTS. Dr. Klingenheben
Interesting case, I have a similar patient with postpartum VF-arrest.
She got an ICD and hat futer TdP-VT documented. Postpartum Cardiac
arrest is almost pathognomonic for LQT-2, as are "notched" T waves.
My opinion is that this particular patient is at high risk for future
events and I clearly would proceed to ICD therapy - irrespective of
future pregnancies. I would add a question to Prof. Priori: are there  
clinical data from
the LQT registry concerning arrhythmic events during/after pregnancy
in patients with suspected/confirmed LQT ?

  Thomas Klingenheben, MD
Assistant Professor of Medicine
Kardiologische Gemeinschaftspraxis
Alfred-Bucherer-Str. 6
D 53115  Bonn - Germany
e-mail: Klingenheben at aol.com
e-mail: Klingenheben at em.uni-frankfurt.de
Web:    www.bonn-kardiologie.de

--
Dr. Sergio Dubner
President of Scientific Committee

Dr. Edgardo Schapachnik
President of Steering Committee