[ARVD-FORUM] Some more remarks. Dr. Marconi
ARVD Symposium
info at arvd-symposium.org
Mon Apr 4 17:00:56 ART 2005
English - Spanish
Undoubtely this is an unusual phatolgy, as well as a pathology of difficult
diagnosis. Therefore we must be aware of the frequency of this desease in
our office.
Marconi Brandão
Cardiologist - CRMRO-1457
--------------------
Sin dudas, esta patologia es inusual, asi como una patologia de dificil
diagnostico. Por lo tanto, debemos estar conscientes de la frecuencia de
esta enfermedad en nuestro consultorio.
Marconi Brandão
Cardiologist - CRMRO-1457
>
> English - Portuguese
>
> In my 25 years as a professional and specialist in cardiology, I only had
> one case of ARVD, approximately 50 years old, and already using ICD and
> amiodarone due to ventricular tachycardias. Do you think it would be
> interesting if I published this? She is clinically well, after suffering an
> emotional bipolar disorder 4 months ago, when she needed to be admitted in
> a Psychiatric Hospital. A medical office case! Warm regards for everyone,
>
> Mesquita
> "Eduardo Mesquita Oliveira" <mesquita at einstein.br>
>
> ------------------------
>
> Em meus 25 anos de formado e especialista em cardiologia, so tenho um caso
> de DAVD, com aproximadamente 50 anos e ja fazendo uso de CDI e amiodarona,
> devido as Taquicardias Ventriculares. Seria interessante eu publicar?
> Clinicamente esta bem, apos ter tido um Transtorno Bipolar emocional ha 4
> meses, necessitando ser internada em Hopital Psiquiatrico. Caso de
> consultorio! Abraços a todos.
>
> Mesquita
> "Eduardo Mesquita Oliveira" <mesquita at einstein.br>
>
> > English - Spanish
> > Dear Guy,
> >
> > We definitely value your opinion and it could well be that the disease is
> > largely underestimated. At least when we compare with number of cases
> > seen clinically of LQTS, HCM, even Brugada syndrome, ARVD is far behind,
> > very rare.
> >
> > But, the virtual symposium is exactly good forum to express such opinions
> > and
> > we appreciate you writing a paragraph on it and we will send your comment
> > to all participants.
> >
> > Best regards
> >
> > Wojciech
> >
> > ----------------------
> >
> > Estimado Guy:
> >
> > Definitivamente valoramos tu opinion y bien podria ser que la enfermedad
> > este enormemente menospreciada. Por lo menos cuando la comparamos con el
> > numero de casos vistos clinicamente de LQTS, CMH, incluso del Sindrome de
> > Brugada, la DAVD esta muy por detras con respecto a las otras, por eso es
> > rara.
> >
> > Pero el Simposio Virtual es exactamente el foro para expresar tales
> > opiniones, y apreciamos que escribas un parrafo al respecto. Nosotros
> > enviaremos tus comentarios a todos los participantes.
> >
> > Saludos cordiales,
> >
> > Wojciech
> >
> >
> > t _______________________________________
> >
> > > English - Spanish
> > >
> > > Dear Wojciech
> > >
> > > I do not agree with the statement that ARVD is a rare disease !
> > >
> > > The histologic substrate of RVD is found in 3.7 % of the general
> > > population
> > >
> > > only few patients are referred to tertiary centers because of
> > > arrhythmias.
> > >
> > > Around 3-5 cases each month are seen in Paris in the Forensic Medicine
> > > Institution
> > >
> > > 10 cases are studied each day !
> > >
> > > In addition many patients have concealed RV dysfunction. This is
> > > visible only in case of independent LV failure
> > > Therefore ARVD and Fat Dissociation Syndrome (see my histopathologic
> > > plates) are important pronostic factors as recently reported.
> > >
> > > Best regards
> > >
> > > Guy
> > >
> > > ----------------
> > >
> > > Estimado Wojciech
> > >
> > > No coincido con la idea de que la DAVD es una enfermedad rara!
> > > El sustrato histologico de DVD se encuentra en el 3,7 % de la poblacion
> > > general, solo unos pocos pacientes son derivados a centros terciarios
> > > debido a arritmias.
> > >
> > > En Paris se ven alrededor de 3-5 casos por mes; en la Forensic Medicine
> > > Institution se estudian 10 casos cada dia!
> > >
> > > Ademas, muchos pacientes tienen disfuncion oculta del VD. Esto solo es
> > > evidente en el caso de insuficiencia independiente del VI.
> > > Por lo tanto, la DAVD y el Sindrome de Disociacion de Adiposidad (ver
> > > mis placas histopatologicas) son factores de pronostico importantes
> > > como se informo recientemente.
> > >
> > > Saludos cordiales,
> > >
> > > Guy
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